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25 résultats

	Pour les 25 documents Envoyer sur ORCID RSS ATOM Exporter BibTeX XML-TEI CSV RTF EndNote PDF HTML Export avancé	Page :	triés par Pertinence Auteur A→Z Auteur Z→A Titre A→Z Titre Z→A Date de publication croissante Date de publication décroissante Date de dépôt croissante Date de dépôt décroissante

		miR-379 links glucocorticoid treatment with mitochondrial response in Duchenne muscular dystrophy Mathilde Sanson , Ai Vu Hong , Emmanuelle Massourides , Nathalie Bourg , Laurence Suel , et al. Scientific Reports, 2020, 10 (1), pp.9139. ⟨10.1038/s41598-020-66016-7⟩ Article dans une revue inserm-02881214v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		A Mouse Model for Monitoring Calpain Activity under Physiological and Pathological Conditions Marc Bartoli , Nathalie Bourg , Daniel Stockholm , F. Raynaud , Antony Delevacque , et al. Journal of Biological Chemistry, 2006, 281 (51), pp.39672-39680. ⟨10.1074/jbc.M608803200⟩ Article dans une revue hal-03674304v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Cis -splicing and Translation of the Pre- Trans -splicing Molecule Combine With Efficiency in Spliceosome-mediated RNA Trans -splicing François Monjaret , Nathalie Bourg , Laurence Suel , Carinne Roudaut , Florence Le Roy , et al. Molecular Therapy, 2014, 22 (6), pp.1176-1187. ⟨10.1038/mt.2014.35⟩ Article dans une revue hal-02336897v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Co-Administration of Simvastatin Does Not Potentiate the Benefit of Gene Therapy in the mdx Mouse Model for Duchenne Muscular Dystrophy Nathalie Bourg , Ai Vu Hong , William Lostal , Abbass Jaber , Nicolas Guerchet , et al. International Journal of Molecular Sciences, 2022, 23 (4), ⟨10.3390/ijms23042016⟩ Article dans une revue hal-03585553v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Dlk1-Dio3 cluster miRNAs regulate mitochondrial functions in Duchenne muscular dystrophy Ai Vu Hong , Nathalie Bourg , Peggy Sanatine , Jerome Poupiot , Karine Charton , et al. Life Science Alliance, 2022, ⟨10.26508/lsa.202201506⟩ Article dans une revue hal-03454735v2	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Different outcome of sarcoglycan missense mutation between human and mouse Sara F Henriques , Cécile Patissier , Nathalie Bourg , Chiara Fecchio , Doriana Sandona , et al. PLoS ONE, 2018, 13 (1), pp.e0191274. ⟨10.1371/journal.pone.0191274⟩ Article dans une revue hal-02333031v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Identification of thiostrepton as a pharmacological approach to rescue misfolded alpha-sarcoglycan mutant proteins from degradation Lucile Hoch , Sara F Henriques , Celine Bruge , Justine Marsolier , Manon Benabides , et al. Scientific Reports, 2019, 9 (1), ⟨10.1038/s41598-019-43399-w⟩ Article dans une revue hal-02138777v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		NF-kappa B-dependent expression of the antiapoptotic factor c-FLIP is regulated by calpain 3, the protein involved in limb-girdle muscular dystrophy type 2A Beatrice Benayoun , Stephen Baghdiguian , Alicia Lajmanovich , Marc Bartoli , Nathalie Danièle , et al. FASEB Journal, 2008, 22 (5), pp.1521-1529. ⟨10.1096/fj.07-8701com⟩ Article dans une revue hal-01610041v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Dual Effects of Exercise in Dysferlinopathy Olivier Biondi , Marie Villemeur , Alice Marchand , Fabrice Chrétien , Nathalie Bourg , et al. American Journal of Pathology, 2013, 182 (6), pp.2298-2309. ⟨10.1016/j.ajpath.2013.02.045⟩ Article dans une revue hal-02338049v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		NF‐NF ‐κ BB‐dependent expression of the antiapoptotic factor c‐FLIP is regulated by calpain 3, the protein involved in limb‐girdle muscular dystrophy type 2A Béatrice Benayoun , Stephen Baghdiguian , Alicia Lajmanovich , Marc Bartoli , Nathalie Daniele , et al. FASEB Journal, 2008, 22 (5), pp.1521-1529. ⟨10.1096/fj.07-8701com⟩ Article dans une revue hal-03674309v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		The Phenotype of Dysferlin-Deficient Mice Is Not Rescued by Adeno-Associated Virus–Mediated Transfer of Anoctamin 5 Florence Le Roy , Laurence Suel , Jérôme Poupiot , Marc Bartoli , François Monjaret , et al. Human gene therapy. Clinical development, 2013, 24 (2), pp.65-76. ⟨10.1089/humc.2012.217⟩ Article dans une revue hal-02336935v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Titin splicing regulates cardiotoxicity associated with calpain 3 gene therapy for limb-girdle muscular dystrophy type 2A William Lostal , Carinne Roudaut , Marine Faivre , Karine Charton , Laurence Suel , et al. Science Translational Medicine, 2019, 11 (520), pp.eaat6072. ⟨10.1126/scitranslmed.aat6072⟩ Article dans une revue hal-03335723v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		A comparison of AAV strategies distinguishes overlapping vectors for efficient systemic delivery of the 6.2 kb Dysferlin coding sequence Marina Pryadkina , William Lostal , Nathalie Bourg , Karine Charton , Carinne Roudaut , et al. Molecular Therapy - Methods and Clinical Development, 2015, 2, pp.15009. ⟨10.1038/mtm.2015.9⟩ Article dans une revue hal-02336876v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Dual Blockade of Misfolded Alpha-Sarcoglycan Degradation by Bortezomib and Givinostat Combination Lucile Hoch , Nathalie Bourg , Fanny Degrugillier , Céline Bruge , Manon Benabides , et al. Frontiers in Pharmacology, 2022, 13, ⟨10.3389/fphar.2022.856804⟩ Article dans une revue hal-03874719v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Species-specific titin splicing regulates cardiotoxicity associated with calpain 3 gene therapy for limb-girdle muscular dystrophy 2A William Lostal , Carinne Roudaut , Marine Faivre , Karine Charton , Laurence Suel , et al. Science Translational Medicine, 2019, 11 (520), pp.eaat6072. ⟨10.1126/scitranslmed.aat6072⟩ Article dans une revue hal-02408897v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		γ-sarcoglycan and dystrophin mutation spectrum in an Algerian cohort Evelyne Gicquel , Natacha Maizonnier , Steven Foltz , William Martin , Nathalie Bourg , et al. Muscle & nerve. Supplement., 2017, 56 (1), pp.129-135. ⟨10.1002/mus.25443⟩ Article dans une revue hal-02333075v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Cardiac ankyrin repeat protein is a marker of skeletal muscle pathological remodelling Lydie Laure , Laurence Suel , Carinne Roudaut , Nathalie Bourg , Ahmed Ouali , et al. FEBS Journal, 2009, 276 (3), pp.669-684. ⟨10.1111/j.1742-4658.2008.06814.x⟩ Article dans une revue hal-01610040v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Efficient recovery of dysferlin deficiency by dual adeno-associated vector-mediated gene transfer William Lostal , Marc Bartoli , Nathalie Bourg , Carinne Roudaut , Azéddine Bentaib , et al. Human Molecular Genetics, 2010, 19 (10), pp.1897-1907. ⟨10.1093/hmg/ddq065⟩ Article dans une revue istex hal-01610036v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Calcium-dependent plasma membrane repair requires m- or mu-calpain, but not calpain-3, the proteasome, or caspases Ronald L. Mellgren , Katsuya Miyake , Irina Kramerova , Melissa J. Spencer , Nathalie Bourg , et al. Biochimica et Biophysica Acta - Molecular Cell Research, 2009, 1793 (12), pp.1886-1893. ⟨10.1016/j.bbamcr.2009.09.013⟩ Article dans une revue hal-01610039v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Assessment of Therapeutic Potential of a Dual AAV Approach for Duchenne Muscular Dystrophy Sonia Albini , Laura Palmieri , Auriane Dubois , Nathalie Bourg , William Lostal , et al. International Journal of Molecular Sciences, 2023, 24 (14), pp.11421. ⟨10.3390/ijms241411421⟩ Article dans une revue hal-04302872v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		A mouse model for monitoring calpain activity under physiological and pathological conditions Marc Bartoli , Nathalie Bourg , Daniel Stockholm , Fabrice Raynaud , Antony Delevacque , et al. Journal of Biological Chemistry, 2006, 281 (51), pp.39672-39680. ⟨10.1074/jbc.M608803200⟩ Article dans une revue hal-01610049v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		A Naturally Occurring Human Minidysferlin Protein Repairs Sarcolemmal Lesions in a Mouse Model of Dysferlinopathy Martin Krahn , Nicolas Wein , Marc Bartoli , William Lostal , Sebastien Courrier , et al. Science Translational Medicine, 2010, 2 (50), ⟨10.1126/scitranslmed.3000951⟩ Article dans une revue hal-01610037v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Lack of Correlation between Outcomes of Membrane Repair Assay and Correction of Dystrophic Changes in Experimental Therapeutic Strategy in Dysferlinopathy William Lostal , Marc Bartoli , Carinne Roudaut , Nathalie Bourg , Martin Krahn , et al. PLoS ONE, 2012, 7 (5), ⟨10.1371/journal.pone.0038036⟩ Article dans une revue hal-01610028v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		A new pathway encompassing calpain 3 and its newly identified substrate cardiac ankyrin repeat protein is involved in the regulation of the nuclear factor‐κB pathway in skeletal muscle Lydie Laure , Nathalie Danièle , Laurence Suel , Sylvie Marchand , Sophie Aubert , et al. FEBS Journal, 2010, 277 (20), pp.4322-4337. ⟨10.1111/j.1742-4658.2010.07820.x⟩ Article dans une revue hal-01610035v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		AAV-mediated transfer of FKRP shows therapeutic efficacy in a murine model but requires control of gene expression Evelyne Gicquel , Natacha Maizonnier , Steven Foltz , William Martin , Nathalie Bourg , et al. Human Molecular Genetics, 2017, 26 (10), pp.1952-1965. ⟨10.1093/hmg/ddx066⟩ Article dans une revue hal-02177575v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More

Filtrer vos résultats

miR-379 links glucocorticoid treatment with mitochondrial response in Duchenne muscular dystrophy

A Mouse Model for Monitoring Calpain Activity under Physiological and Pathological Conditions

Cis -splicing and Translation of the Pre- Trans -splicing Molecule Combine With Efficiency in Spliceosome-mediated RNA Trans -splicing

Co-Administration of Simvastatin Does Not Potentiate the Benefit of Gene Therapy in the mdx Mouse Model for Duchenne Muscular Dystrophy

Dlk1-Dio3 cluster miRNAs regulate mitochondrial functions in Duchenne muscular dystrophy

Different outcome of sarcoglycan missense mutation between human and mouse

Identification of thiostrepton as a pharmacological approach to rescue misfolded alpha-sarcoglycan mutant proteins from degradation

NF-kappa B-dependent expression of the antiapoptotic factor c-FLIP is regulated by calpain 3, the protein involved in limb-girdle muscular dystrophy type 2A

Dual Effects of Exercise in Dysferlinopathy

NF‐NF ‐κ BB‐dependent expression of the antiapoptotic factor c‐FLIP is regulated by calpain 3, the protein involved in limb‐girdle muscular dystrophy type 2A

The Phenotype of Dysferlin-Deficient Mice Is Not Rescued by Adeno-Associated Virus–Mediated Transfer of Anoctamin 5

Titin splicing regulates cardiotoxicity associated with calpain 3 gene therapy for limb-girdle muscular dystrophy type 2A

A comparison of AAV strategies distinguishes overlapping vectors for efficient systemic delivery of the 6.2 kb Dysferlin coding sequence

Dual Blockade of Misfolded Alpha-Sarcoglycan Degradation by Bortezomib and Givinostat Combination

Species-specific titin splicing regulates cardiotoxicity associated with calpain 3 gene therapy for limb-girdle muscular dystrophy 2A

γ-sarcoglycan and dystrophin mutation spectrum in an Algerian cohort

Cardiac ankyrin repeat protein is a marker of skeletal muscle pathological remodelling

Efficient recovery of dysferlin deficiency by dual adeno-associated vector-mediated gene transfer

Calcium-dependent plasma membrane repair requires m- or mu-calpain, but not calpain-3, the proteasome, or caspases

Assessment of Therapeutic Potential of a Dual AAV Approach for Duchenne Muscular Dystrophy

A mouse model for monitoring calpain activity under physiological and pathological conditions

A Naturally Occurring Human Minidysferlin Protein Repairs Sarcolemmal Lesions in a Mouse Model of Dysferlinopathy

Lack of Correlation between Outcomes of Membrane Repair Assay and Correction of Dystrophic Changes in Experimental Therapeutic Strategy in Dysferlinopathy

A new pathway encompassing calpain 3 and its newly identified substrate cardiac ankyrin repeat protein is involved in the regulation of the nuclear factor‐κB pathway in skeletal muscle

AAV-mediated transfer of FKRP shows therapeutic efficacy in a murine model but requires control of gene expression