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AIF-regulated oxidative phosphorylation supports lung cancer development
Shuan Rao
,
Laura Mondragón
,
Blanka Pranjic
,
Toshikatsu Hanada
,
Gautier Stoll
,
et al.
Article dans une revue
hal-02355955v1
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Yeast cells lacking the mitochondrial gene encoding the ATP synthase subunit 6 exhibit a selective loss of complex IV and unsual mitochondrial morphology
M. Rak
,
E. Tétaud
,
F. Godard
,
I. Sagot
,
B. Salin
,
et al.
Journal of Biological Chemistry, 2007, 282 ((15)), pp.10853-64
Article dans une revue
hal-00131733v1
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Biochemical consequences in yeast of the human mitochondrial DNA8993T>C mutation in the ATPase6 gene found in NARP/MILS patients
R. Kucharczyk
,
M. Rak
,
J.P. Di Rago
Biochimica et Biophysica Acta (BBA) - Reviews on Bioenergetics, 2009, 1793 (5), pp.817-24
Article dans une revue
hal-00366403v1
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Mitochondrial ATP synthase disorders: Molecular mechanisms and the quest for curative therapeutic approaches.
R. Kucharczyk
,
M. Zick
,
M. Bietenhader
,
M. Rak
,
E. Couplan
,
et al.
BBA - Biochimica et Biophysica Acta, 2009, 1793 (1), pp.186-199
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hal-00324961v1
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Succinate Dehydrogenase, Succinate, and Superoxides: A Genetic, Epigenetic, Metabolic, Environmental Explosive Crossroad
Paule Bénit
,
Judith Goncalves
,
Riyad El Khoury
,
Malgorzata Rak
,
Judith Favier
,
et al.
Article dans une revue
hal-03830056v1
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Mitochondria are physiologically maintained at close to 50 °C
Dominique Chrétien
,
Paule Bénit
,
Hyung-Ho Ha
,
Susanne Keipert
,
Riyad El-Khoury
,
et al.
Article dans une revue
inserm-02136777v1
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Arabidopsis thaliana alternative dehydrogenases: a potential therapy for mitochondrial complex I deficiency? Perspectives and pitfalls
Alessia Catania
,
Arcangela Iuso
,
Juliette Bouchereau
,
Laura S Kremer
,
Marina Paviolo
,
et al.
Article dans une revue
hal-02414326v1
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Distinctive Krebs cycle remodeling in iPSC-derived neural and mesenchymal stem cells
Sarah Benlamara
,
Laetitia Aubry
,
Julien Fabregue
,
Paule Bénit
,
Pierre Rustin
,
et al.
Article dans une revue
hal-02414270v1
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Paradoxical inhibition of glycolysis by pioglitazone opposes the mitochondriopathy caused by AIF deficiency
Paule Bénit
,
Alice Pelhaître
,
Elise Saunier
,
Sylvie Bortoli
,
Assetou Coulibaly
,
et al.
Article dans une revue
inserm-01477508v1
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A 'petite obligate' mutant of Saccharomyces cerevisiae : functional mDNA is lethal in cells lacking the delta subunit of mitochondrial F1-ATPase
S. Duvezin-Caubet
,
M. Rak
,
L. Lefebvre-Legendre
,
E. Tétaud
,
N. Bonnefoy
,
et al.
Journal of Biological Chemistry, 2006, 281 (24), pp.16305-13
Article dans une revue
hal-00068656v1
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Depletion of WFS1 compromises mitochondrial function in hiPSC-derived neuronal models of Wolfram syndrome
Malgorzata Zatyka
,
Tatiana Rosenstock
,
Congxin Sun
,
Adina Palhegyi
,
Georgina Hughes
,
et al.
Article dans une revue
hal-04309147v1
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Cyanide resistant respiration and the alternative oxidase pathway: A journey from plants to mammals
Riyad El-Khoury
,
Malgorzata Rak
,
Paule Bénit
,
Howard Jacobs
,
Pierre Rustin
Article dans une revue
hal-03830054v1
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A new threat identified in the use of SDHIs pesticides targeting the mitochondrial succinate dehydrogenase enzyme
Paule Benit
,
Sylvie Bortoli
,
Laurence Huc
,
Manuel Schiff
,
Anne-Paule Gimenez-Roqueplo
,
et al.
2018
Pré-publication, Document de travail
hal-02789139v1
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A "petite obligate" mutant of Saccharomyces cerevisiae: functional mtDNA is lethal in cells lacking the delta subunit of mitochondrial F1-ATPase.
Stéphane Duvezin-Caubet
,
Malgorzata Rak
,
Linnka Lefebvre-Legendre
,
Emmanuel Tetaud
,
Nathalie Bonnefoy
,
et al.
Article dans une revue
hal-00132178v1
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The pathogenic m.8993 T > G mutation in mitochondrial ATP6 gene prevents proton release from the subunit c -ring rotor of ATP synthase
Xin Su
,
Alain Dautant
,
Malgorzata Rak
,
François Godard
,
Nahia Ezkurdia
,
et al.
Article dans une revue
hal-03830051v1
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Deregulating mitochondrial metabolite and ion transport has beneficial effects in yeast and human cellular models for NARP syndrome
Xin Su
,
Malgorzata Rak
,
Emmanuel Tetaud
,
François Godard
,
Elodie Sardin
,
et al.
Article dans une revue
hal-02362008v1
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Increasing mitochondrial substrate-level phosphorylation can rescue respiratory growth of an ATP synthase deficient yeast.
C. Schwimmer
,
L. Lefebvre-Legendre
,
M. Rak
,
A. Devin
,
P.P. Slonimski
,
et al.
Journal of Biological Chemistry, 2005, 280 (35), pp.30751-30759
Article dans une revue
hal-00069229v1
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Yeast models of human mitochondrial diseases : from molecular mechanisms to drug screening
C. Schwimmer
,
M. Rak
,
L. Lefebvre-Legendre
,
S. Duvezin-Caubet
,
G. Plane
,
et al.
Biotechnology Journal, 2006, 1 (3), pp.270-281
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hal-00068718v1
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A yeast model of the neurogenic ataxia retinitis pigmentosa (NARP) T8993G mutation in the mitochondrial ATP synthase-6 gene.
M. Rak
,
E. Tétaud
,
S. Duvezin-Caubet
,
N. Ezkurdia
,
M. Bietenhader
,
et al.
Journal of Biological Chemistry, 2007, 282 ((47)), pp.34039-47
Article dans une revue
hal-00173414v1
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SLC25A32 Mutations and Riboflavin-Responsive Exercise Intolerance
M. Schiff
,
A. Veauville-Merllie
,
C. H. Su
,
A. Tzagoloff
,
M. Rak
,
et al.
Article dans une revue
hal-01850416v1
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Evolutionarily conserved susceptibility of the mitochondrial respiratory chain to SDHI pesticides and its consequence on the impact of SDHIs on human cultured cells
Paule Bénit
,
Agathe Kahn
,
Dominique Chretien
,
Sylvie Bortoli
,
Laurence Huc
,
et al.
Article dans une revue
inserm-02409310v1
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Pitfalls in Monitoring Mitochondrial Temperature Using Charged Thermosensitive Fluorophores
Dominique Chretien
,
Paule Bénit
,
Christine Leroy
,
Riyad El-Khoury
,
Sunyou Park
,
et al.
Article dans une revue
hal-03092858v1
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SLC13A3 variants cause acute reversible leukoencephalopathy and α-ketoglutarate accumulation
Joseph Dewulf
,
Elsa Wiame
,
Imen Dorboz
,
Monique Elmaleh-Bergès
,
Apolline A Imbard
,
et al.
Article dans une revue
hal-02414351v1
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Depletion of WFS1 compromises mitochondrial function in hiPSC-derived neuronal models of Wolfram syndrome
Malgorzata Zatyka
,
Tatiana Rosenstock
,
Congxin Sun
,
Adina Palhegyi
,
Georgina Hughes
,
et al.
Article dans une revue
hal-04307211v1
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ZIKA virus elicits P53 activation and genotoxic stress in human neural progenitors similar to mutations involved in severe forms of genetic microcephaly and p53
Vincent El Ghouzzi
,
Federico Bianchi
,
Ivan Molineris
,
Bryan Mounce
,
Gaia Berto
,
et al.
Article dans une revue
hal-02323045v1
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