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	Pour les 25 documents Envoyer sur ORCID RSS ATOM Exporter BibTeX XML-TEI CSV RTF EndNote PDF HTML Export avancé	Page :	triés par Pertinence Auteur A→Z Auteur Z→A Titre A→Z Titre Z→A Date de publication croissante Date de publication décroissante Date de dépôt croissante Date de dépôt décroissante

		Yeast cells lacking the mitochondrial gene encoding the ATP synthase subunit 6 exhibit a selective loss of complex IV and unsual mitochondrial morphology M. Rak , E. Tétaud , F. Godard , I. Sagot , B. Salin , et al. Journal of Biological Chemistry, 2007, 282 ((15)), pp.10853-64 Article dans une revue hal-00131733v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		AIF-regulated oxidative phosphorylation supports lung cancer development Shuan Rao , Laura Mondragón , Blanka Pranjic , Toshikatsu Hanada , Gautier Stoll , et al. Cell Research, 2019, 29 (7), pp.579-591. ⟨10.1038/s41422-019-0181-4⟩ Article dans une revue hal-02355955v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Arabidopsis thaliana alternative dehydrogenases: a potential therapy for mitochondrial complex I deficiency? Perspectives and pitfalls Alessia Catania , Arcangela Iuso , Juliette Bouchereau , Laura S Kremer , Marina Paviolo , et al. Orphanet Journal of Rare Diseases, 2019, 14 (1), pp.236. ⟨10.1186/s13023-019-1185-3⟩ Article dans une revue hal-02414326v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Distinctive Krebs cycle remodeling in iPSC-derived neural and mesenchymal stem cells Sarah Benlamara , Laetitia Aubry , Julien Fabregue , Paule Bénit , Pierre Rustin , et al. Biochemical and Biophysical Research Communications, 2019, 511 (3), pp.658-664. ⟨10.1016/j.bbrc.2019.02.033⟩ Article dans une revue hal-02414270v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Paradoxical inhibition of glycolysis by pioglitazone opposes the mitochondriopathy caused by AIF deficiency Paule Bénit , Alice Pelhaître , Elise Saunier , Sylvie Bortoli , Assetou Coulibaly , et al. EBioMedicine, 2017, pp.S2352-3964(17)30072-5. ⟨10.1016/j.ebiom.2017.02.013⟩ Article dans une revue inserm-01477508v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Biochemical consequences in yeast of the human mitochondrial DNA8993T>C mutation in the ATPase6 gene found in NARP/MILS patients R. Kucharczyk , M. Rak , J.P. Di Rago Biochimica et Biophysica Acta (BBA) - Reviews on Bioenergetics, 2009, 1793 (5), pp.817-24 Article dans une revue hal-00366403v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Mitochondrial ATP synthase disorders: Molecular mechanisms and the quest for curative therapeutic approaches. R. Kucharczyk , M. Zick , M. Bietenhader , M. Rak , E. Couplan , et al. BBA - Biochimica et Biophysica Acta, 2009, 1793 (1), pp.186-199 Article dans une revue hal-00324961v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Succinate Dehydrogenase, Succinate, and Superoxides: A Genetic, Epigenetic, Metabolic, Environmental Explosive Crossroad Paule Bénit , Judith Goncalves , Riyad El Khoury , Malgorzata Rak , Judith Favier , et al. Biomedicines, 2022, 10 (8), pp.1788. ⟨10.3390/biomedicines10081788⟩ Article dans une revue hal-03830056v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Mitochondria are physiologically maintained at close to 50 °C Dominique Chrétien , Paule Bénit , Hyung-Ho Ha , Susanne Keipert , Riyad El-Khoury , et al. PLoS Biology, 2018, 16 (1), pp.e2003992. ⟨10.1371/journal.pbio.2003992⟩ Article dans une revue inserm-02136777v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		The pathogenic m.8993 T > G mutation in mitochondrial ATP6 gene prevents proton release from the subunit c -ring rotor of ATP synthase Xin Su , Alain Dautant , Malgorzata Rak , François Godard , Nahia Ezkurdia , et al. Human Molecular Genetics, 2021, 30 (5), pp.381-392. ⟨10.1093/hmg/ddab043⟩ Article dans une revue hal-03830051v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Deregulating mitochondrial metabolite and ion transport has beneficial effects in yeast and human cellular models for NARP syndrome Xin Su , Malgorzata Rak , Emmanuel Tetaud , François Godard , Elodie Sardin , et al. Human Molecular Genetics, 2019, 28 (22), pp.3792-3804. ⟨10.1093/hmg/ddz160⟩ Article dans une revue hal-02362008v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Increasing mitochondrial substrate-level phosphorylation can rescue respiratory growth of an ATP synthase deficient yeast. C. Schwimmer , L. Lefebvre-Legendre , M. Rak , A. Devin , P.P. Slonimski , et al. Journal of Biological Chemistry, 2005, 280 (35), pp.30751-30759 Article dans une revue hal-00069229v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Yeast models of human mitochondrial diseases : from molecular mechanisms to drug screening C. Schwimmer , M. Rak , L. Lefebvre-Legendre , S. Duvezin-Caubet , G. Plane , et al. Biotechnology Journal, 2006, 1 (3), pp.270-281 Article dans une revue hal-00068718v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		A yeast model of the neurogenic ataxia retinitis pigmentosa (NARP) T8993G mutation in the mitochondrial ATP synthase-6 gene. M. Rak , E. Tétaud , S. Duvezin-Caubet , N. Ezkurdia , M. Bietenhader , et al. Journal of Biological Chemistry, 2007, 282 ((47)), pp.34039-47 Article dans une revue hal-00173414v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Cyanide resistant respiration and the alternative oxidase pathway: A journey from plants to mammals Riyad El-Khoury , Malgorzata Rak , Paule Bénit , Howard Jacobs , Pierre Rustin Biochimica biophysica acta (BBA) - Bioenergetics, 2022, 1863 (6), pp.148567. ⟨10.1016/j.bbabio.2022.148567⟩ Article dans une revue hal-03830054v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		A new threat identified in the use of SDHIs pesticides targeting the mitochondrial succinate dehydrogenase enzyme Paule Benit , Sylvie Bortoli , Laurence Huc , Manuel Schiff , Anne-Paule Gimenez-Roqueplo , et al. 2018 Pré-publication, Document de travail hal-02789139v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		A 'petite obligate' mutant of Saccharomyces cerevisiae : functional mDNA is lethal in cells lacking the delta subunit of mitochondrial F1-ATPase S. Duvezin-Caubet , M. Rak , L. Lefebvre-Legendre , E. Tétaud , N. Bonnefoy , et al. Journal of Biological Chemistry, 2006, 281 (24), pp.16305-13 Article dans une revue hal-00068656v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		A "petite obligate" mutant of Saccharomyces cerevisiae: functional mtDNA is lethal in cells lacking the delta subunit of mitochondrial F1-ATPase. Stéphane Duvezin-Caubet , Malgorzata Rak , Linnka Lefebvre-Legendre , Emmanuel Tetaud , Nathalie Bonnefoy , et al. Journal of Biological Chemistry, 2006, 281 (24), pp.16305-13. ⟨10.1074/jbc.M513805200⟩ Article dans une revue hal-00132178v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Depletion of WFS1 compromises mitochondrial function in hiPSC-derived neuronal models of Wolfram syndrome Malgorzata Zatyka , Tatiana Rosenstock , Congxin Sun , Adina Palhegyi , Georgina Hughes , et al. Stem Cell Reports, 2023, 18 (5), pp.1090-1106. ⟨10.1016/j.stemcr.2023.04.002⟩ Article dans une revue hal-04309147v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		ZIKA virus elicits P53 activation and genotoxic stress in human neural progenitors similar to mutations involved in severe forms of genetic microcephaly and p53 Vincent El Ghouzzi , Federico Bianchi , Ivan Molineris , Bryan Mounce , Gaia Berto , et al. Cell Death and Disease, 2016, 7, pp.e2440. ⟨10.1038/cddis.2016.266⟩ Article dans une revue hal-02323045v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		SLC25A32 Mutations and Riboflavin-Responsive Exercise Intolerance M. Schiff , A. Veauville-Merllie , C. H. Su , A. Tzagoloff , M. Rak , et al. New England Journal of Medicine, 2016, 374 (8), pp.795-7. ⟨10.1056/NEJMc1513610⟩ Article dans une revue hal-01850416v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Evolutionarily conserved susceptibility of the mitochondrial respiratory chain to SDHI pesticides and its consequence on the impact of SDHIs on human cultured cells Paule Bénit , Agathe Kahn , Dominique Chretien , Sylvie Bortoli , Laurence Huc , et al. PLoS ONE, 2019, 14 (11), pp.e0224132. ⟨10.1371/journal.pone.0224132⟩ Article dans une revue inserm-02409310v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Pitfalls in Monitoring Mitochondrial Temperature Using Charged Thermosensitive Fluorophores Dominique Chretien , Paule Bénit , Christine Leroy , Riyad El-Khoury , Sunyou Park , et al. Chemosensors, 2020, 8 (4), pp.124. ⟨10.3390/chemosensors8040124⟩ Article dans une revue hal-03092858v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		SLC13A3 variants cause acute reversible leukoencephalopathy and α-ketoglutarate accumulation Joseph Dewulf , Elsa Wiame , Imen Dorboz , Monique Elmaleh-Bergès , Apolline A Imbard , et al. Annals of Neurology, 2019, 85 (3), pp.385-395. ⟨10.1002/ana.25412⟩ Article dans une revue hal-02414351v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More
		Depletion of WFS1 compromises mitochondrial function in hiPSC-derived neuronal models of Wolfram syndrome Malgorzata Zatyka , Tatiana Rosenstock , Congxin Sun , Adina Palhegyi , Georgina Hughes , et al. Stem Cell Reports, 2023, 18 (5), pp.1090-1106. ⟨10.1016/j.stemcr.2023.04.002⟩ Article dans une revue hal-04307211v1	Envoyer sur ORCID Exporter BibTeX XML-TEI Dublin Core DC Terms EndNote DataCite Export avancé Partager Gmail Facebook X LinkedIn More

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Yeast cells lacking the mitochondrial gene encoding the ATP synthase subunit 6 exhibit a selective loss of complex IV and unsual mitochondrial morphology

AIF-regulated oxidative phosphorylation supports lung cancer development

Arabidopsis thaliana alternative dehydrogenases: a potential therapy for mitochondrial complex I deficiency? Perspectives and pitfalls

Distinctive Krebs cycle remodeling in iPSC-derived neural and mesenchymal stem cells

Paradoxical inhibition of glycolysis by pioglitazone opposes the mitochondriopathy caused by AIF deficiency

Biochemical consequences in yeast of the human mitochondrial DNA8993T>C mutation in the ATPase6 gene found in NARP/MILS patients

Mitochondrial ATP synthase disorders: Molecular mechanisms and the quest for curative therapeutic approaches.

Succinate Dehydrogenase, Succinate, and Superoxides: A Genetic, Epigenetic, Metabolic, Environmental Explosive Crossroad

Mitochondria are physiologically maintained at close to 50 °C

The pathogenic m.8993 T > G mutation in mitochondrial ATP6 gene prevents proton release from the subunit c -ring rotor of ATP synthase

Deregulating mitochondrial metabolite and ion transport has beneficial effects in yeast and human cellular models for NARP syndrome

Increasing mitochondrial substrate-level phosphorylation can rescue respiratory growth of an ATP synthase deficient yeast.

Yeast models of human mitochondrial diseases : from molecular mechanisms to drug screening

A yeast model of the neurogenic ataxia retinitis pigmentosa (NARP) T8993G mutation in the mitochondrial ATP synthase-6 gene.

Cyanide resistant respiration and the alternative oxidase pathway: A journey from plants to mammals

A new threat identified in the use of SDHIs pesticides targeting the mitochondrial succinate dehydrogenase enzyme

A 'petite obligate' mutant of Saccharomyces cerevisiae : functional mDNA is lethal in cells lacking the delta subunit of mitochondrial F1-ATPase

A "petite obligate" mutant of Saccharomyces cerevisiae: functional mtDNA is lethal in cells lacking the delta subunit of mitochondrial F1-ATPase.

Depletion of WFS1 compromises mitochondrial function in hiPSC-derived neuronal models of Wolfram syndrome

ZIKA virus elicits P53 activation and genotoxic stress in human neural progenitors similar to mutations involved in severe forms of genetic microcephaly and p53

SLC25A32 Mutations and Riboflavin-Responsive Exercise Intolerance

Evolutionarily conserved susceptibility of the mitochondrial respiratory chain to SDHI pesticides and its consequence on the impact of SDHIs on human cultured cells

Pitfalls in Monitoring Mitochondrial Temperature Using Charged Thermosensitive Fluorophores

SLC13A3 variants cause acute reversible leukoencephalopathy and α-ketoglutarate accumulation

Depletion of WFS1 compromises mitochondrial function in hiPSC-derived neuronal models of Wolfram syndrome