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NRF2 signaling cascade in amyotrophic lateral sclerosis: bridging the gap between promise and reality
Pauline Tarot
,
Christelle Lasbleiz
,
Jean-Charles Liévens
Article dans une revue
hal-04436982v1
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Sigma-1 receptor: culprit and rescuer in motor neuron diseases
Jean-Charles Liévens
,
Tangui Maurice
Article dans une revue
hal-02996077v1
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Increased energy metabolism rescues glia-induced pathology in a Drosophila model of Huntington's disease.
Marie-Thérèse Besson
,
Pascale Dupont
,
Yih-Woei C Fridell
,
Jean-Charles Liévens
Article dans une revue
hal-00625236v1
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Expanded polyglutamine peptides disrupt EGF receptor signaling and glutamate transporter expression in Drosophila
J. C. Lievens
,
T. Rival
,
M. Iche
,
H. Chneiweiss
,
S. Birman
Human Molecular Genetics, 2005, 14, pp.713-724
Article dans une revue
hal-00118469v1
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Glycolysis upregulation is neuroprotective as a compensatory mechanism in ALS
Ernesto Manzo
,
Ileana Lorenzini
,
Dianne Barrameda
,
Abigail O'Conner
,
Jordan Barrows
,
et al.
Article dans une revue
hal-03005486v1
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Sigma-1 receptor chaperones rescue nucleocytoplasmic transport deficit seen in cellular and Drosophila ALS/FTD models
Pin-Tse Lee
,
Jean-Charles Liévens
,
Shao-Ming Wang
,
Jian-Ying Chuang
,
Bilal Khalil
,
et al.
Article dans une revue
hal-02990866v1
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Morphological, behavioral and cellular analyses revealed different phenotypes in Wolfram syndrome wfs1a and wfs1b zebrafish mutant lines
Lucie Crouzier
,
Elodie Richard
,
Camille Diez
,
Hala Alzaeem
,
Morgane Denus
,
et al.
Article dans une revue
hal-03757700v1
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PINK1-induced mitophagy promotes neuroprotection in Huntington’s disease
Bilal Khalil
,
Najla El Fissi
,
Aicha Aouane
,
Marie-Jeanne Cabirol-Pol
,
Thomas Rival
,
et al.
Article dans une revue
hal-01787280v1
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Huntington chorea in Drosophila and mice: toward new therapeutic steps.
J.C. Lievens
,
S. Birman
Médecine/Sciences, 2003, 19, pp.593-599
Article dans une revue
hal-00310975v1
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Mitochondrial quality control in amyotrophic lateral sclerosis: towards a common pathway?
Bilal Khalil
,
Jean-Charles Liévens
Article dans une revue
hal-01998697v1
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Enhanced Neuronal Glucose Transporter Expression Reveals Metabolic Choice in a HD Drosophila Model
Marie Thérèse Besson
,
Karin Alegría
,
Pamela Garrido-Gerter
,
Luis Felipe Barros
,
Jean-Charles Liévens
Article dans une revue
hal-01218042v1
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The Drosophila inner-membrane protein PMI controls crista biogenesis and mitochondrial diameter.
Marc Macchi
,
Najla El Fissi
,
Roberta Tufi
,
Mélanie Bentobji
,
Jean-Charles Liévens
,
et al.
Article dans une revue
hal-00843395v1
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Astrocytes in Huntington's chorea: accomplice or guilty of the neuronal death?
S. Birman
,
J.C. Lievens
Médecine/Sciences, 2007, 23, pp.845-849
Article dans une revue
hal-00310867v1
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Sigma-1 receptor is a key genetic modulator in amyotrophic lateral sclerosis
Simon Couly
,
Bilal Khalil
,
Véronique Viguier
,
Julien Roussel
,
Tangui Tm Maurice
,
et al.
Article dans une revue
hal-02360092v1
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Reducing canonical Wingless/Wnt signaling pathway confers protection against mutant Huntingtin toxicity in Drosophila.
Pascale Dupont
,
Marie-Thérèse Besson
,
Jérôme Devaux
,
Jean-Charles Liévens
Article dans une revue
istex
hal-00701180v1
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AKT-sensitive or insensitive pathways of toxicity in glial cells and neurons in Drosophila models of Huntington's disease
M. Iche
,
S. Birman
,
J.C. Lievens
,
M. Laval
,
C. Faivre-Sarrailh
Human Molecular Genetics, 2008, 17, pp.882-894
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hal-00310865v1
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Activation of the sigma-1 receptor chaperone alleviates symptoms of Wolfram syndrome in preclinical models
Lucie Crouzier
,
Alberto Danese
,
Yuko Yasui
,
Elodie Richard
,
Jean-Charles Liévens
,
et al.
Article dans une revue
hal-03757649v1
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Enhancing Mitofusin/Marf ameliorates neuromuscular dysfunction in Drosophila models of TDP-43 proteinopathies
Bilal Khalil
,
Marie-Jeanne Cabirol-Pol
,
Laetitia Miguel
,
Alexander J. Whitworth
,
Magalie Lecourtois
,
et al.
Article dans une revue
hal-01994093v1
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Sigma-1 receptor agonist PRE-084 confers protection against TAR DNA-binding protein-43 toxicity through NRF2 signalling
Christelle Lasbleiz
,
Amandine Peyrel
,
Pauline Tarot
,
Jérôme Sarniguet
,
Lucie Crouzier
,
et al.
Article dans une revue
hal-04210325v1
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